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CASE REPORT article
Front. Urol.
Sec. Pediatric, Adolescent and Developmental Urology
Volume 4 - 2024 |
doi: 10.3389/fruro.2024.1456889
Rare Developmental Urological Disease: A Case Report of Zinner Syndrome
Provisionally accepted- Kunming Medical University, Kunming, China
Zinner syndrome (ZS) is a rare congenital urologic disorder characterized by a classic triad of manifestations: ipsilateral seminal vesicle cyst, ipsilateral ejaculatory duct obstruction, and ipsilateral renal hypoplasia. We present a case of a young male patient diagnosed with ZS and treated at our center. Imaging revealed absence of the left kidney, along with enlarged, dysmorphic, and abnormally dilated seminal vesicle glands, as well as multiple tortuous tubular extensions of the seminal vesicles into the bladder. Cystoscopy confirmed the presence of a cystic mass in the bladder with elongated seminal vesicles. Semen analysis, biochemical indices, and tumor markers showed no significant abnormalities. In this post, we present a case of ZS with abdominal pain as the primary symptom.The patient underwent laparoscopic left nephroureterectomy and recovered well postoperatively, with regular follow-up provided thereafter.We discuss its pathogenesis, diagnosis, and treatment, and provide a literature review of the disease.
Keywords: male infertility, Male mesonephric abnormalities, diagnosis, Zinner syndrome, Treatment
Received: 29 Jun 2024; Accepted: 10 Dec 2024.
Copyright: © 2024 Shi, Duan, Bi, Yang, Zhang, Wang, Luo, Lu, Yang, Yang, Ran and Zhao. This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) or licensor are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
* Correspondence:
Jianpeng Zhang, Kunming Medical University, Kunming, China
Qiao Wang, Kunming Medical University, Kunming, China
Zongyan Luo, Kunming Medical University, Kunming, China
Yong Yang, Kunming Medical University, Kunming, China
Fengming Ran, Kunming Medical University, Kunming, China
Bin Zhao, Kunming Medical University, Kunming, China
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