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CASE REPORT article

Front. Pediatr.
Sec. Pediatric Surgery
Volume 12 - 2024 | doi: 10.3389/fped.2024.1429537

Case Report: Management of a Congenital Intrahepatic Portosystemic Shunt with Portal Vein Aneurysm in a Child Using 3D Computer-Assisted Partial Right Hepatectomy

Provisionally accepted
Johan Arief Johan Arief 1,2Yao Liu Yao Liu 1,2*Wenli Xiu Wenli Xiu 1,2Xiwei Hao Xiwei Hao 1*Feifei Wang Feifei Wang 2*Nan Xia Nan Xia 2,3*Qian Dong Qian Dong 1,2*
  • 1 Department of Pediatric Surgery, Affiliated Hospital of Qingdao University, Qingdao, Shandong Province, China
  • 2 Shandong Key Laboratory of Digital Medicine and Computer Assisted Surgery, Affiliated Hospital of Qingdao University, Qingdao, Shandong Province, China
  • 3 Institute for Digital Medicine and Computer-assisted Surgery in Qingdao University, Qingdao, China

The final, formatted version of the article will be published soon.

    Congenital portosystemic shunts (CPSS) are rare pediatric vascular malformations characterized by abnormal development of the portal vein, which is attributed to incomplete embryonic remodeling of the hepatic and surrounding vasculature. CPSS manifests in two main forms: intrahepatic and extrahepatic. This study details the management of a pediatric patient diagnosed with Congenital Intrahepatic Portosystemic Shunt (CIPS) who was referred to our institution. By using a computer-assisted surgical system, the right hepatectomy was successfully performed, guided by precise intraoperative navigation based on three-dimensional reconstructions of enhanced CT imagery. The patient exhibited a favorable postoperative recovery trajectory, with the absence of complications or recurrence throughout the monitoring period.

    Keywords: Congenital intrahepatic portosystemic shunt, Aneurysm, 3D computer assisted surgery, case report, Partial right hepatectomy

    Received: 08 May 2024; Accepted: 10 Oct 2024.

    Copyright: © 2024 Arief, Liu, Xiu, Hao, Wang, Xia and Dong. This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY). The use, distribution or reproduction in other forums is permitted, provided the original author(s) or licensor are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.

    * Correspondence:
    Yao Liu, Department of Pediatric Surgery, Affiliated Hospital of Qingdao University, Qingdao, Shandong Province, China
    Xiwei Hao, Department of Pediatric Surgery, Affiliated Hospital of Qingdao University, Qingdao, Shandong Province, China
    Feifei Wang, Shandong Key Laboratory of Digital Medicine and Computer Assisted Surgery, Affiliated Hospital of Qingdao University, Qingdao, Shandong Province, China
    Nan Xia, Shandong Key Laboratory of Digital Medicine and Computer Assisted Surgery, Affiliated Hospital of Qingdao University, Qingdao, Shandong Province, China
    Qian Dong, Department of Pediatric Surgery, Affiliated Hospital of Qingdao University, Qingdao, Shandong Province, China

    Disclaimer: All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.