AUTHOR=Chan Yat Chi , Kan Amanda N. C. , Yuen Liz Y. P. , Wan Innes Y. P. , Fung Kevin K. F. , Cheung Yiu-fai , Leung Karen K. Y. , Ku Dennis T. L. , Liu Anthony P. Y. TITLE=Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome JOURNAL=Frontiers in Pediatrics VOLUME=10 YEAR=2022 URL=https://www.frontiersin.org/journals/pediatrics/articles/10.3389/fped.2022.885068 DOI=10.3389/fped.2022.885068 ISSN=2296-2360 ABSTRACT=

Low-grade fibromyxoid sarcomas (LGFMSs) are typically adult-onset tumors that arise from the extremities. Here, we report an exceptional case of primary thoracic LGFMS in an 8-year-old girl that resulted in mediastinal syndrome. In reporting this case, we discuss the clinical challenges, role of molecular profiling and review reported cases of pediatric thoracic LGFMSs.