AUTHOR=McLennan Daniel I. , Solano Elyan C. Ruiz , Handler Stephanie S. , Lincoln Joy , Mitchell Michael E. , Kirkpatrick Edward C. 

TITLE=Pulmonary Vein Stenosis: Moving From Past Pessimism to Future Optimism

JOURNAL=Frontiers in Pediatrics

VOLUME=9

YEAR=2021

URL=https://www.frontiersin.org/journals/pediatrics/articles/10.3389/fped.2021.747812

DOI=10.3389/fped.2021.747812

ISSN=2296-2360

ABSTRACT=<p>Pulmonary Vein Stenosis (PVS) is a rare disease with a prevalence of around 1. 7 cases per 100,000 children under 2 years old. Treatment options for this disease have not provided great results and pathophysiology of this condition is still poorly understood. Here, we will review the history of PVS including diagnostic tools and treatments, the current management approach, and what the future holds for this devastating disease.</p>