AUTHOR=Kadakia Nevil , Lobritto Steven J. , Ovchinsky Nadia , Remotti Helen E. , Yamashiro Darrell J. , Emond Jean C. , Martinez Mercedes TITLE=A Challenging Case of Hepatoblastoma Concomitant with Autosomal Recessive Polycystic Kidney Disease and Caroli Syndrome—Review of the Literature JOURNAL=Frontiers in Pediatrics VOLUME=5 YEAR=2017 URL=https://www.frontiersin.org/journals/pediatrics/articles/10.3389/fped.2017.00114 DOI=10.3389/fped.2017.00114 ISSN=2296-2360 ABSTRACT=

We report a rare case of an 18-month-old female with autosomal recessive polycystic kidney disease, Caroli syndrome, and pure fetal type hepatoblastoma. The liver tumor was surgically resected with no chemotherapy given. Now 9 years post resection she demonstrates no local or distant recurrence and stable renal function.