AUTHOR=Cossío-Aranda Jorge , Aranda-Frausto Alberto , Berarducci Joaquin , Espinola-Zavaleta Nilda , González-Melchor Laila , Vázquez-Antona Clara , Meléndez-Ramirez Gabriela , Armenta-Moreno Javier Ivan , Keirns Candace TITLE=Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma JOURNAL=Frontiers in Cardiovascular Medicine VOLUME=8 YEAR=2021 URL=https://www.frontiersin.org/journals/cardiovascular-medicine/articles/10.3389/fcvm.2021.709328 DOI=10.3389/fcvm.2021.709328 ISSN=2297-055X ABSTRACT=

We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-mortem immunochemistry studies of both tumors led to the diagnosis of a primary malignant cardiac PEComa with histopathologic characteristics that resembled a rhabdomyoma with abundant “spider cells.”